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Definition of Uroporphyrinogen
1. Noun. (biochemistry) Any of a class of tetrapyrroles with four propionic acid groups and four acetic acid groups, involved in the synthesis of porphyrin. ¹
¹ Source: wiktionary.com
Medical Definition of Uroporphyrinogen
1. See: porphyrinogens. Uroporphyrinogen decarboxylase, an enzyme that participates in haem biosynthesis; it catalyses the decarboxylation of uroporphyrinogen III to produce coproporphyrinogen III; it also acts on uroporphyrinogen I; a deficiency of this enzyme will result in either porphyria cutanea tarda or hepatoerythropoietic porphyria. Uroporphyrinogen III cosynthase, an enzyme in haem biosynthesis that participates in the formation of uroporphyrinogen III; a deficiency of this protein results in congenital erythropoietic porphyria. (05 Mar 2000)