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Medical Definition of Saccharopine
1. HOOC(CH2)2CH(COOH)NH(CH2)4CH(NH2)COOH;a derivative of alpha-ketoglutarate and l-lysine that is an intermediate in l-lysine catabolism; elevated in cases of saccharopinuria. (05 Mar 2000)
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1. HOOC(CH2)2CH(COOH)NH(CH2)4CH(NH2)COOH;a derivative of alpha-ketoglutarate and l-lysine that is an intermediate in l-lysine catabolism; elevated in cases of saccharopinuria. (05 Mar 2000)