|
|
Medical Definition of Schilder's disease
1. Term used to describe at least two separate disorders described by Schilder: 1) Diffuse sclerosis or encephalitis periaxialis diffusa; a nonfamilial disorder affecting primarily children and young adults and characterised by progressive dementia, visual disturbances, deafness, pseudobulbar palsy, and hemiplegia or quadriplegia. Most patients die within a few years of onset; pathologically, there is a large, asymmetrical area of myelin destruction, sometimes involving an entire cerebral hemisphere, and typically with extension across the corpus callosum. 2) The leukodystrophies. Synonym: encephalitis periaxialis diffusa, Flatau-Schilder disease. (05 Mar 2000)
Lexicographical Neighbors of Schilder's Disease
Other Resources:
