Definition of Hirschsprung's disease
1. Noun. Congenital condition in which the colon does not have the normal network of nerves; there is little urge to defecate so the feces accumulate and cause megacolon.
Medical Definition of Hirschsprung's disease
1.
A congenital condition which results in an enlarged and poorly functioning colon due to abnormal intestinal motility. These patients are at risk for intestinal obstruction. Constipation, vomiting, abdominal distention, poor weight gain, a retarded growth are common. Treatment include the use of a temporary colostomy with later resection of the affected portion of bowel.
Symptoms are eliminated in up to 90% of patients after surgery. Outcomes are better with early intervention.
Aganglionosis of myenteric plexus of colon, functional obstruction, aganglionic segment of normal caliber, continuous involvement, from rectum proximally, males (80%), usually presents by 6 weeks, complications: enterocolitis, perforation, associated with Down syndrome Differential diagnosis: ileal atresia, meconium ileus (no air-fluid levels)
(27 Sep 1997)
Lexicographical Neighbors of Hirschsprung's Disease
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