Medical Definition of Phenylalanine 4-monooxygenase

1. An enzyme that catalyses the oxidation of l-phenylalanine to l-tyrosine with O2 and tetrahydrobiopterin (the latter forming the dihydro derivative) which is reduced by NADPH and a reductase to the active form; a deficiency of either of these enzymes will result in phenylketonuria. Synonym: phenylalanine 4-hydroxylase. (05 Mar 2000)

Lexicographical Neighbors of Phenylalanine 4-monooxygenase

phenyl
phenylacetaldehyde dehydrogenase
phenylacetamide
phenylacetate - CoA ligase
phenylacetic acid
phenylaceturic acid
phenylacetylurea
phenylacrylic acid
phenylacrylic acid decarboxylase
phenylalaninase
phenylalanine
phenylalanine
phenylalanine-tRNA ligase
phenylalanines
phenylalanine 4-hydroxylase
phenylalanine 4-monooxygenase (current term)
phenylalanine aminopeptidase
phenylalanine ammonia lyase
phenylalanine hydroxylase
phenylalanine hydroxylase phosphatase
phenylalanine oxidase
phenylalanyl-arginyl-aminopeptidase
phenylalanyl chain
phenylamine
phenylamine
phenylbenzene
phenylbutazone
phenylbutazone
phenylbutazones
phenylcarbinol

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