Medical Definition of Nephroblastomatosis
1.
Persistent primitive renal tissue (normally present up to 36 weeks), potential precursor to Wilms tumour: present in 30% of kidneys with single and 100% of kidneys with bilateral Wilms tumour associated with: hemihypertrophy, sporadic aniridia, pseudohermaphroditism, Klippel-Trenaunay syndrome, Beckwith-Wiedemann syndrome, splenic agenesis with hepatic malformation findings: kidneys may be enlarged, deformity of the pelvocalyceal system, ultrasound: subtle subcapsular nodules (hypo-/iso-/hyperechoic), CT: hypodense subcapsular nodules after contrast enhancement
(12 Dec 1998)
Lexicographical Neighbors of Nephroblastomatosis
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