Medical Definition of Medium-chain acyl-CoA dehydrogenase
1.
Deficiency in mitochondrial beta oxidation of fatty acids gives a disorder frequently masquerading as reye syndrome or sudden infant death; leads to buildup of octanoyl carnitine in urine
Registry number: EC 1.3.-
Synonym: mcaca-dehydrogenase, medium-chain acyl-coenzyme a dehydrogenase, octanoyl-CoA dehydrogenase, mcad enzyme
(26 Jun 1999)
Lexicographical Neighbors of Medium-chain Acyl-CoA Dehydrogenase
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