Medical Definition of Lysyl hydroxylase
1.
An enzyme that acts on specific lysyl residues in certain proteins (e.g., collagens) with alpha-ketoglutarate and O2 to produce d-hydroxylysyl residues, succinate, and CO2; this enzyme, which requires Fe2+ and ascorbate, is deficient in Ehlers-Danlos syndrome type VI.
Synonym: lysyl 2-oxoglutarate dioxygenase.
(05 Mar 2000)
Lexicographical Neighbors of Lysyl Hydroxylase
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