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Medical Definition of Juvenile hyalin fibromatosis
1. A rare recessively inherited deforming disorder of head, neck, and generalised cutaneous nodules or tumours in children with normal mentality; the lesions consist of fibroblasts separated by an eosinophilic hyalin stroma composed mostly of glycosaminoglycans. Synonym: systemic hyalinosis. (05 Mar 2000)