Medical Definition of Iduronidase
1.
An enzyme that hydrolyzes iduronosidic linkages in desulfated dermatan. Deficiency of this enzyme produces hurler's syndrome.
Chemical name: Glycosaminoglycan alpha-L-iduronohydrolase
Registry number: EC 3.2.1.76
(12 Dec 1998)
Lexicographical Neighbors of Iduronidase
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