Medical Definition of Fumarylacetoacetate

1. HOOCCH=CHCOCH2COCH2COOH;an intermediate in phenylalanine and tyrosine catabolism; elevated in tyrosinaemia IA. Fumarylacetoacetate hydrolase, an enzyme that catalyses the hydrolysis of fumarylacetoacetate to fumarate and acetoacetate; a deficiency indicates tyrosinaemia IA. (05 Mar 2000)

Lexicographical Neighbors of Fumarylacetoacetate

Fumaria claviculata
Fumaria fungosa
Fumaria officinalis
Fumaria sempervirens
fumaric
fumaric
fumaric acid
fumaric acid
fumaric acidemia
fumaric aminase
fumaric hydrogenase
fumarine
fumarole
fumaroles
fumarolic
fumarylacetoacetate (current term)
fumatories
fumatory
fumble
fumble
fumbled
fumbler
fumblers
fumbles
fumbling
fumblingly
fume
fume
fumed
fumed oak

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