Medical Definition of Congenital dyserythropoietic anaemia

1. A group of autosomal recessive anaemia's characterised by ineffective erythropoiesis, bone marrow erythroblastic multinuclearity, and secondary haemochromatosis. Three types are described: Type I, macrocytic, megaloblastic anaemia with erythroblastic internuclear chromatin bridges, type II,, normoblastic anaemia with multinucleated erythroblasts, type III, macrocytic anaemia with erythroblastic multinuclearity and gigantoblasts. (05 Mar 2000)

Lexicographical Neighbors of Congenital Dyserythropoietic Anaemia

congenital atonic pseudoparalysis
congenital baldness
congenital bronchiectasis
congenital cardiomyopathy
congenital cataract
congenital cerebellar atrophy
congenital cerebral aneurysm
congenital choreoathetosis
congenital clasped thumb with mental retardation
congenital conus
congenital defect
congenital defect
congenital diaphragmatic hernia
congenital disease
congenital disorder
congenital dyserythropoietic anaemia (current term)
congenital dysphagocytosis
congenital dysplasia of the hip
congenital dysplastic angiectasia
congenital dysplastic angiomatosis
congenital ectodermal defect
congenital ectodermal dysplasia
congenital elephantiasis
congenital epulis of newborn
congenital erythropoietic porphyria
congenital facial diplegia
congenital fibrosis of the extraocular muscles
congenital generalised fibromatosis
congenital giant pigmented nevus
congenital glaucoma

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