Medical Definition of Aminoadipic d-semialdehyde synthase

1. A bifunctional enzyme used in lysine degradation; it has a lysine:alpha-ketoglutarate reductase activity as well as a saccharopine dehydrogenase activity. A deficiency of this enzyme results in familial hyperlysinaemia. (05 Mar 2000)

Lexicographical Neighbors of Aminoadipic D-semialdehyde Synthase

amino-terminal residue
aminoacetic acid
aminoacetonitrile
aminoacid-tRNA ligases
aminoacidemia
aminoaciduria
aminoaciduria
aminoacidurias
aminoacridines
aminoacyl
aminoacyl-tRNA
aminoacyl-tRNA synthetases
aminoacylase
aminoacyltransferases
aminoacyl adenylate
aminoadipic d-semialdehyde synthase (current term)
aminoadipic semialdehyde synthase
aminoalkane
aminoalkanoic acid
aminobenzene
aminobenzine
aminobenzoic acid
aminobiphenyl compounds
aminobutyric acids
aminocaproic acid
aminocarbonyl
aminocarboxylic acid
aminocitric acid
aminodeoxychorismate lyase
aminodeoxychorismate synthase

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