Medical Definition of Ornithine transcarbamoylase
1.
An enzyme of the transferase class that catalyses the reaction of carbamoyl phosphate and l-ornithine to yield orthophosphate and l-citrulline. The enzyme occurs in the liver. The reaction is a part of the urea cycle. Genetic deficiency of the enzyme, an x-linked trait, impairs urea formation and produces hyperammonaemia.
Chemical name: Carbamoyl-phosphate:L-ornithine carbamoyltransferase
Registry number: EC 2.1.3.3
(12 Dec 1998)
Lexicographical Neighbors of Ornithine Transcarbamoylase
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