Definition of Maleylacetoacetate

1. Noun. (biochemistry) An intermediate in the metabolism of tyrosine. ¹

¹ Source: wiktionary.com

Medical Definition of Maleylacetoacetate

1. An intermediate in l-phenylalanine and l-tyrosine catabolism; accumulates in certain inherited disorders of tyrosine metabolism. Maleylacetoacetate cis,trans-isomerase, an enzyme that catalyses the reversible conversion of maleylacetoacetate to 4-fumarylacetoacetate; an enzyme that participates in l-tyrosine catabolism; a deficiency of this enzyme is associated with tyrosinaemia type IB. Structure: -OOC-CH==CH-COCH2COCH2COO- (05 Mar 2000)

Lexicographical Neighbors of Maleylacetoacetate

malet
maletreat
maletreated
maletreating
maletreats
malevolence
malevolences
malevolency
malevolent
malevolent program
malevolently
malevolous
malexecution
maleyl
maleylacetate reductase
maleylacetoacetate (current term)
maleylacetoacetic acid
maleylpyruvate isomerase
malfatti
malfeasance
malfeasances
malfeasant
malfeasants
malfeasor
malfeasors
malfed
malformation
malformations
malformed
malformedness

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