Medical Definition of Dejerine-sottas disease

1. A familial type of demyelinating sensorimotor polyneuropathy that begins in early childhood and is slowly progressive; clinically characterised by foot pain and paresthesias, followed by symmetrical weakness and wasting of the distal limbs; one of the causes of stork legs; patients are wheelchair bound at an early age; peripheral nerves are palpably enlarged and non-tender; pathologically, onion bulb formation is seen in the nerves: whorls of overlapping, intertwined Schwann cell processes that encircle bare axons; usually autosomal recessive inheritance. Synonym: Dejerine's disease, progressive hypertrophic polyneuropathy. (05 Mar 2000)

Lexicographical Neighbors of Dejerine-sottas Disease

Deists
Deiters
Deiters' cells
Deiters' nucleus
Deiters' terminal frames
Dejerine
Dejerine's disease
Dejerine's hand phenomenon
Dejerine's reflex
Dejerine's sign
Dejerine-Klumpke
Dejerine-Klumpke palsy
Dejerine-Klumpke syndrome
Dejerine-Lichtheim phenomenon
Dejerine-Roussy syndrome
Dejerine-Sottas disease
Dekker
Del
Del Boy
Del Castillo
Del Rio
Delacroix
Delafield
Delafield's haematoxylin
Delairea
Delairea odorata
Delaney
Delaney clause
Delaware

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