Medical Definition of ATP cobalamin adenoxyltransferase

1. An enzyme that catalyses the reaction of ATP, water, and cobalamin to form orthophosphate, pyrophosphate, and adenoxylcobalamin. Adenosylcobalamin is required by methylmalonyl-CoA mutase. A deficiency of ATP cobalamin adenosyltransferase will lead to methylmalonic acidemia. (05 Mar 2000)

Lexicographical Neighbors of ATP Cobalamin Adenoxyltransferase

ATMs
ATN
ATO
ATOC
ATOL
ATP
ATP-corrinoid adenosyltransferase
ATP-dependent DNA strand transferase
ATP-diphosphatase
ATP-monophosphatase
ATP-ubiquitin-dependent proteinase
ATPD
ATPS
ATP citrate (pro-3S)-lyase
ATP citrate lyase
ATP cobalamin adenoxyltransferase (current term)
ATP dependent 26S protease
ATP phosphoribosyltransferase
ATP sulfurylase
ATP synthase
ATPase
ATPases
ATRA
ATSB
ATT site
ATV
ATW
ATWS
AT content
AU

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